Abstract. ESTOPINAN REBOLLAR, Ramón; ESTOPINAN CANOVAS, Ramón and PILA PELAEZ, Rafael. Enfermedad de Hirschsprung en un adulto. Rev Col. Resumen. LOMBANA, Luis Jorge y DOMINGUEZ, Luis Carlos. Surgery in adult Hirschsprung’s disease. Rev Col Gastroenterol [online]. , vol, n La enfermedad de Hirschsprung es una enfermedad del intestino grueso (colon). Normalmente, las heces fecales son empujadas a través del colon por.

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Only cases of HD have been ehfermedad in adults, with male predominance in a 4: Zonal adult Hirschsprung’s disease.

Hirschsprung’s Disease HDalso known as congenital aganglionic megacolon, is an anomaly characterized by an absence of ganglion cells in the myenteric and submucosal plexuses in a variable bowel segment. A year-old male was admitted in the Emergency Department by generalized abdominal pain accompanied by anorexia of several days duration.

Vólvulo en adultos

It can cause symptoms of severe chronic constipation or frequent episodes of fecal impaction. Rev Esp Enferm Dig, 3pp. Enfermedad de Hirschsprung del adulto: Nevertheless, the literature considers as the procedure of choice the Duhamel technique in only one surgical time, 2 which reduces the hospitalization time.

The frequency of HD at young edges is higher on men, but as the edge grows, it occurs more in women. Female patient, 13 years old, coming from Campo Grande – MS, reports that since birth had intestinal constipation, with mean bowel movements at every days with hardened feces, being followed-up by a pediatrician and in treatment for functional constipation. Hirschsprung Disease HD or Congenital Megacolon is an anomaly that is characterized mainly for the absence of ganglion cells in the myenteric plexus and submucosal in a variable segment of the intestine.


Other proposed mechanisms include defects in the neuroblast differentiation and accelerated destruction of ganglion cells in the intestine 4.

Symptoms had worsened in recent months, prompting her to seek the evaluation of a proctologist. The Congenital Megacolon presents agonglionosis in different lengths of the intestine; many times associated to other congenital anomalies. CT scan was performed, showing signs of peritonitis caused by dehiscence of ileum-rectal suture.

Barium enema showing megarectum. After 24 hours, the patient presented hemodynamic instability, with severe abdominal pain. Complaints of fecal incontinence are often reported in the literature in cases of functional constipation and of idiopathic megacolon.

No abnormalities resulted from the rectal examination. Conventional enfermefad manometry trace showing the absence of the inhibitory rectoanal reflex with the maximum tolerable rectal capacity. Enfermedad de Hirschsprung en un adulto.

The journal accepts original articles, scientific letters, review articles, clinical guidelines, consensuses, editorials, letters to the Editors, brief communications, and clinical images in Gastroenterology in Spanish and English for their publication. We can conclude that HD is a rare entity in adults and should be suspected in patients with megacolon with a history of constipation refractory to treatment since childhood. This segment is everted and extracted by transanal way.

Hirschsprung’s disease as a rare cause of refractory constipation in an adult patient.

Vólvulo en adultos | HCA Healthcare

Fifty per cent of the patients are younger than 30 years of age hirschzprung. These radiological images were ed with Hirschsprung’s disease; for this reason, we extracted surgically the fecal mass through the anus.

Surgical treatment for the disease was described in Adult Hirschsprung’s disease diagnosed during forensic autopsy. A resection of distal rectal mucosa of the aganglionic segment is performed, maintaining muscular wall of this segment. Abdomen was very distended and tympanic, with previous laparotomy scar, painful on palpation diffusely. The diagnosis of HD is supported by barium enema studies, anorectal manometry and rectal biopsy.


This item has received. Department of General and Digestive Surgery. In this case, the aganglionic segment is not removed, but a rear dissection is performed.

Niger J Clin Pract ; In se case, we are in a situation of irreversible dilatation of entire colon, so we opted for a total colectomy, restoring intestinal transit by ileo-rectal anastomosis. Hirschsprung disease with debut in adult age as acute intestinal obstruction: HD presents itself by symptoms of constipation, such as a greater than h delay in elimination of meconium, abdominal distention and vomiting.

Most cases become manifest during the neonatal period, but in rare instances, this disease is initially diagnosed in adult age. Niger J Clin Pract. The pathologist’s report showed the existence of ulceration foci with acute inflammation in the submucosa.

Enfermedad de Hirschprung del adulto

Si continua navegando, consideramos que acepta su uso. Its etiology is unknown, although it is considered multifactorial.

The disease rarely presents as an acute intestinal obstruction. SNIP measures contextual citation impact by wighting citations based on the total number of hirschslrung in a subject field.